Publicaciones científicas

Idiopathic mediastinal fibrosis associated with hypercoagulability: a case report

01-dic-2001 | Revista: Anales de Medicina Interna

Bauzá Alonso A, García Gómez JP, Abades Vázquez C, García González N, Prieto Valtueña J.


Mediastinal fibrosis is a rare and unknown disease characterized by the presence of a fibrotic mass in the anterior mediastinum that can invade close structures as gullet, trachea, recurrent nerve, superior cava vein etc. Only 1-2% of patients with mediastinal fibrosis associate superior cava vein obstruction. When it appears, it is produced by extrinsic compression for fibrotic magma in almost all the cases.

A case of hypercoagulability disorder associated with mediastinal fibrosis and superior cava vein obstruction by thrombosis (intrinsec mechanism), and the satisfactory evolution after the treatment with oral anticoagulation, corticosteroids and tamoxifen is presented.

CITA DEL ARTÍCULO An Med Interna. 2001 Dec;18(12):638-40